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AANEM Connect | Hirayama Disease of late onset in females? View modes: 
Benjamin Sucher - 4/12/2019 4:28:47 PM
Hirayama Disease of late onset in females?
I had a 2nd case (in 2-3 years) of monomelic amyotrophy, this one a 67 y/o female, 4 month onset of weakness and wasting in her left hand - no numbness, tingling or pain, and minimal chronic neck pain (non-radiating).  Totally normal sensory studies but low amplitude (ulnar worse than radial) or unobtainable (median) motor responses, and marked denervation in T1>C8>C7 (and paraspinals).  Awaiting C&T spine MRIs.  Is anyone else seeing these kinds of cases? 

There is an article in Muscle & Nerve from January 2008 about this, authored by Patel, Knepper, and Jones.  Volume 37; pp115-119

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